Dentogenesis Imperfecta (DI)

Osteogenesis Imperfecta (OI) is always associated with fragile bones but may also affect the growth of the jaws and teeth. Approximately half of people diagnosed with OI have normally developed teeth, and their ongoing care includes routine exam and cleanings. No additional precautions are necessary for treatment beyond what would be normally considered.

However, some also present as a tooth defect called Dentinogeneisis Imperfecta (DI), sometimes referred to as “Brittle Teeth”. Individuals with this condition may have misshapen or discolored teeth that chip or break easily and require special care. All teeth may not be equally affected with DI.

 

Dental Care for Patients with Dentinogeneisis Imperfecta

DI may be identified as early as appearance of the first baby tooth at approximately 6 months to 1 year. X-rays may also be useful in corroborating the clinical findings, as some changes below the gumline are not visible on exam. Primary teeth are usually more affected than permanent teeth, and regular care is needed to maintain teeth as long as possible.

Patients with DI will require more regular exams to monitor for cracking, chipping, and wear of teeth. Brushing and dental cleanings have been demonstrated to be safe but will not make teeth affected by DI whiter. Bleaching is not advised, because the discoloration is due to enamel staining, but rather underlying dentin.

The Osteogenesis Imperfecta Foundation, Inc. (OI Foundation) is the only voluntary national health organization dedicated to helping people cope with the problems associated with osteogenesis imperfecta.